{"id":7360,"date":"2020-10-12T13:12:07","date_gmt":"2020-10-12T12:12:07","guid":{"rendered":"https:\/\/euromedic.rs\/pregledi\/hirurgija\/minimalno-invazivna-hirurgija\/gerb-gastroezofagealna-refluksna-bolest-minimalno-invazivna-hirurgija-gornjeg-digestivnog-trakta-copy\/"},"modified":"2020-10-12T13:21:46","modified_gmt":"2020-10-12T12:21:46","slug":"gist-gastrointestinalni-stromalni-tumori-minimalno-invazivna-hirurgija-gornjeg-digestivnog-trakta","status":"publish","type":"post","link":"https:\/\/euromedic.rs\/pregledi\/hirurgija\/minimalno-invazivna-hirurgija\/gist-gastrointestinalni-stromalni-tumori-minimalno-invazivna-hirurgija-gornjeg-digestivnog-trakta\/","title":{"rendered":"GIST (Gastrointestinalni stromalni tumori) &#8211; Minimalno invazivna hirurgija gornjeg digestivnog trakta"},"content":{"rendered":"<p><b>Gastrointestinalni stromalni tumori (GIST)<\/b><span style=\"font-weight: 400;\"> su naj\u010de\u0161\u0107i mezenhimalni tumori gastrointestinalnog trakta, visokog malignog potencijala. Karakteri\u0161u se izuzetnim \u0161arenilom u klini\u010dkim, histopatolo\u0161kim i genetskim osobinama i predstavljaju naj\u010des\u0107e mezenhimalne tumore gastrointestinalnog trakta. Lokalizacija im je naj\u010de\u0161\u0107e na \u017eelucu (60%) i tankom crevu (25-30%), a re\u0111e na debelom crevu (&lt; 5%), jednjaku (&lt; 3%) i zavr\u0161nom segmentu debelog creva (rektumu) i anusu (&lt; 5%).\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b>Epidemiologija<\/b><span style=\"font-weight: 400;\">\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b>U\u010destalost<\/b><span style=\"font-weight: 400;\">\u00a0<\/span><\/p>\n<p><span style=\"font-weight: 400;\">U\u010destalost GIST u Sjedinjenim Dr\u017eavama, Evropi i Aziji je skoro identi\u010dna i kre\u0107e se od 1 do 20 slu\u010daja na milion stanovnika, svake godine.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b>Mortalitet\/morbiditet<\/b><span style=\"font-weight: 400;\">\u00a0<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Kona\u010dni ishod bolesti kod bolesnika sa GIST umnogome zavisi od te\u017eine klini\u010dke slike, manifestacija i patohistolo\u0161kih osobina tumora. Petogodi\u0161nja stopa pre\u017eivljavanja bolesnika sa GIST kre\u0107e se od 28 do 60 posto. Stopa pre\u017eivljavanja mo\u017ee biti razli\u010dita od bolesnika do bolesnika na \u0161ta uti\u010de lokalizacija primarnih promena, stepen malignosti i metastaski potencijal. Prose\u010dna du\u017eina pre\u017eivljavanja u grupi lokalizovanih tumora je 5 godina, dok je srednja du\u017eina pre\u017eivljavanja u grupi sa metatstaskim promenama oko 10 do 20 meseci. Ve\u0107e formacije GIST su povezane sa \u010destim komplikacijama kao \u0161to su krvarenja u gastrointestinalnom traktu, opstrukcije (ileus) i perforacija creva.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"font-weight: 400;\">Tumori GIST se mogu klasificirati u visoko i nisko rizi\u010dne na osnovu veli\u010dine tumora i mitotske aktivnosti. Opisane karakteristike tumora uvek se razmatraju u prognozi i tuma\u010denju patohistolo\u0161kih nalaza.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b>Pol<\/b><\/p>\n<p><span style=\"font-weight: 400;\">GIST su ne\u0161to u\u010destaliji kod mu\u0161karaca nego kod \u017eena, iako su mnogi istra\u017eiva\u010di mi\u0161ljenja da ovi tumori nemaju sklonost prema odre\u0111enom polu.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b>Starost\u00a0<\/b><\/p>\n<p><span style=\"font-weight: 400;\">GIST se naj\u010de\u0161\u0107e dijagnostikuju u drugoj polovini \u0161este ili prvoj polovini sedeme decenije \u017eivota (ili izme\u0111u 55 i 65 godine \u017eivota). Povremeno, GIST se mogu javiti kod u mla\u0111ih odraslih osoba, dok su kod dece jako retki.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b>Etiopatogeneza<\/b><span style=\"font-weight: 400;\">\u00a0<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Etiopatogenetski faktori koji izazivaju gastrointestinalne stromalne tumore (GIST) nisu jasno izdvojeni, a genetsku osnovu je te\u0161ko odrediti jer su oni uglavnom sporadi\u010dni. Me\u0111utim, otkrivene su izvesne genetske i citogenetske aberacije koje se mogu smatrati odgovornim za nastanak GIST.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"font-weight: 400;\">Prema dosada\u0161njim istra\u017eivanjima smatra se da su gastrointestinalni stromalni tumori mezanhimalni tumori, \u010dije \u0107elije vode poreklo od intesticijalne, pejsmejker Cajal \u0107elije, koja poti\u010de od autonomnog nervnog sistema i zadu\u017eena je za regulaciju motiliteta gastrointesinalnog trakta.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b>Klini\u010dka slika<\/b><span style=\"font-weight: 400;\">\u00a0<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Simptomi uzrokovani GIST su kod najve\u0107eg broja bolesnika nespecifi\u010dni. Kod oko 75% bolesnika u klini\u010dkoj slici dominira bol u trbuhu, krvarenje iz gastrointestinalnog trakta (25%), op\u0161ta slabost i malaksalost (24%), dispepsija (16%), pad nivo gvo\u017e\u0111a u serumu sa prate\u0107om anemijom (15%), mu\u010dnina i povra\u0107anje (12%) i zatvor ili proliv (9%). Tumor na \u017eelucu je samo u oko 8% bolesnika opipljiv.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"font-weight: 400;\">U studiji koja je obuhvatila veliki broj bolesnika, najve\u0107i broj simptoma imali su bolesnici u grupi GIST \u010dija je prose\u010dne veli\u010dina tumora bila 6 cm, dok 20% bolesnika sa prose\u010dnom veli\u010dinom tumora do 2 cm, nije imalo simptome.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b>Dijagnostika\u00a0<\/b><\/p>\n<p><span style=\"font-weight: 400;\">Definitivna dijagnoza gastrointestinalnih stromalnih tumora se naj\u010de\u0161\u0107e postavlja nakon operacije i kona\u010dnih patohistolo\u0161kih pregleda. Preoperativno, mo\u017ee se identifikovati nakon endoskopskog pregleda, tuma\u010den od strane iskusnog lekara-endoskopiste. Za preciznije odre\u0111ivanje lokalizacije unutar zida creva, a samim tim i izvesniju dijagnozu, koristi se endoskopski ultrazvuk. CT i NMR pregledi su metode koje svakako pridonose postavljanju dijagnoze GIST-a. Usled dobre prokrvljenosti ovih tumora, biopsiju treba izbegavati kako bi prevenirali krvarenje i mogu\u0107u diseminaciju (\u0161irenje) bolesti.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b>Le\u010denje\u00a0<\/b><\/p>\n<p><span style=\"font-weight: 400;\">Naj\u010de\u0161\u0107e primenjivana i najuspe\u0161nija terapija kod GIST je hirur\u0161ka resekcija. Ve\u0107ina ovih tumora se mo\u017ee le\u010diti na pomenuti na\u010din. Me\u0111utim, kod velikog procenta operisanih nakon hirur\u0161kog le\u010denja (u 20% do 40%) slu\u010dajeva mogu se javiti recidivi. Hirurski tretman je dominantan na\u010din le\u010denja gastrointestinalnih stromalnih tumora \u017eeluca.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"font-weight: 400;\">Pored hirur\u0161ke, u poslednje vreme terapija GIST se sve vi\u0161e kombinuje primenom imatiniba i sunitiniba (blokatorima tirozin kinaznih receptora), naro\u010dito kod recidiviraju\u0107ih i inoperabilnih tumora. Veoma \u010desto zbog nemogu\u0107nosti sprovo\u0111enja adekvatne preoperativne dijagnostike postoji hirurska dilema o stepenu radikalnosti operativnog zahvata, koji umnogome zavisi prvenstveno od stepena maligniteta, ali i drugih parametara. Naj\u010de\u0161\u0107a komplikacija nakon operacije GIST je distalna metastaza tumorskih \u0107elija u jetri.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"font-weight: 400;\">Parametri kao sto su: veli\u010dina tumora, mitotski indeks, prisustvo nekroze, krvarenja u tumoru, infiltracija lokalnih struktura, prisutvo limfogenih i jetrenih metastaza odre\u0111uju stepen maligniteta tumora, i na\u010din daljeg le\u010denja.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"font-weight: 400;\">Nakon otkri\u0107a alteracije gena koje se nalaze u etiologiji GIST, u terapiji rekurentnih i neoperabilnih GIST sve vi\u0161e se koristi imatinib koji selektivno inhibi\u0161e grupu tirozinkinaznih receptora, uklju\u010duju\u0107i KIT i PDGFRA. Adjuvantna i neoadjuvantna terapija imatinibom je za sada u praksi najprihva\u0107enija jer ona pobolj\u0161ava prognozu bolesti i mo\u017ee se koristiti u slu\u010daju odmaklog, rekurentnog i\/ili metastatskog GIST. I pored velike efektivnosti ove terapije i velike bezbednosti njene primene, u pojedinim slu\u010dajevima pojavljivala su se gastrointestinalna i intraabdominalna krvarenja.\u00a0<\/span><\/p>\n<p>&nbsp;<\/p>\n<p><span style=\"font-weight: 400;\">\u0160irom sveta se i dalje neprekidno sprovode istra\u017eivanja koja bi omogu\u0107ila pronala\u017eenje novih i efikasnijih lekova koji bi spre\u010davali rezistentnost GIST na dosada\u0161nju terapiju.<\/span><\/p>\n","protected":false},"excerpt":{"rendered":"<p>Gastrointestinalni stromalni tumori (GIST) su naj\u010de\u0161\u0107i mezenhimalni tumori gastrointestinalnog trakta, visokog malignog potencijala. Karakteri\u0161u se&#8230;<\/p>\n","protected":false},"author":1,"featured_media":7363,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"inline_featured_image":false,"footnotes":""},"categories":[512],"tags":[513],"class_list":["post-7360","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-minimalno-invazivna-hirurgija","tag-minimalno-invazivna-hirurgija"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.2 - https:\/\/yoast.com\/wordpress\/plugins\/seo\/ -->\n<title>Ultrazvuk dijagnostika - Dijagnostika i le\u010denje u Euromediku<\/title>\n<meta name=\"description\" content=\"Gastrointestinalni stromalni tumori (GIST) su naj\u010de\u0161\u0107i mezenhimalni tumori gastrointestinalnog trakta..\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/euromedic.rs\/pregledi\/hirurgija\/minimalno-invazivna-hirurgija\/gist-gastrointestinalni-stromalni-tumori-minimalno-invazivna-hirurgija-gornjeg-digestivnog-trakta\/\" \/>\n<meta property=\"og:locale\" content=\"sr_RS\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Ultrazvuk dijagnostika - 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