{"id":6051,"date":"2020-05-13T15:48:41","date_gmt":"2020-05-13T14:48:41","guid":{"rendered":"https:\/\/euromedic.rs\/pregledi\/neurologija-multipla-skleroza-copy\/"},"modified":"2020-10-07T10:47:18","modified_gmt":"2020-10-07T09:47:18","slug":"neurologija-neuromijelitis-optika","status":"publish","type":"post","link":"https:\/\/euromedic.rs\/pregledi\/specijalisticki-pregledi\/neurologija\/neurologija-neuromijelitis-optika\/","title":{"rendered":"Neurologija &#8211; Neuromijelitis optika"},"content":{"rendered":"<p><span style=\"font-weight: 400;\">Neromijelitis optika spektar bolesti ili NMO spektar bolesti (NMOSD od engl.\u00a0 neuromyelitis optica spectrum disorder) je autoimuna demijelinizaciona bolest (o\u0161te\u0107enje mijelinskog omota\u010da nerava), centralnog nervnog sistema, koja uglavnom zahvata opti\u010dke \u017eivce (opti\u010dki neuritis) i ki\u010dmenu mo\u017edinu ( mijelitis), dok promene na mozgu mogu izostati, ili su atipi\u010dne sa druga\u010dijom anatomskom prezentacijom i oblikom lezija nego kod onih u multiploj sklerozi (MS)\u00a0<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Spektar neuromijelitis optika (NMO) nije oblik MS. Danas se zna da su etiopatogeneza\u00a0 ovog spektra bolesti, patohistolo\u0161ki nalaz lezija, terapija, prognoza,\u00a0 sasvim druga\u010diji nego kod MS.\u00a0<\/span><\/p>\n<p><span style=\"font-weight: 400;\">U NMO spektar spadaju\u00a0 i forme NMO\u00a0 u sklopu drugih bolesti (Ha\u0161imoto tireoiditis, Sistemski eritemski lupus, Sjegrenov sindrom,\u00a0 Miastenija gravis, Diabetes melitus tip 1, Sarkoidoza&#8230;) Analizom uzorka krvi\u00a0 mo\u017ee se\u00a0 identifikovati\u00a0 specifi\u010dan biomarker\u00a0 za NMO &#8211; antitela na akvaporin 4\u00a0 (anti AQP4 Ig at). Ova antitela ne postoje kod obolelih od\u00a0 MS\u00a0 a prisutna su u\u00a0 oko 70 % obolelih od\u00a0 NMO spektra. Dakle kod 30-ak % obolelih od NMO spektra nema ovog antitela ali se kod tre\u0107ine od njih mo\u017ee identifikovati antitelo na MOG ( autoantitela na mijelinski oligodendrocitni glikoproteina). Kada se ne mogu identifikovati pomenuta antitela, dijagnoza oboljenja iz NMO spektra\u00a0 se postavlja na osnovu\u00a0 klini\u010dkih karakteristika,\u00a0 dodatnih zahteva\u00a0 nalaza\u00a0 na MR pregledu mozga i ki\u010dmene mo\u017edine., te isklju\u010denjem alternativnih dijagnoza.\u00a0\u00a0<\/span><\/p>\n<p><strong>Koji su simptomi NMO spektra bolesti?<\/strong><\/p>\n<p><span style=\"font-weight: 400;\">Bolest se ispoljava zamu\u0107enim vidom, bolom u oku ili oba oka, promenom percepcije boje, te razli\u010ditim stepenom gubitka vida. Zbog o\u0161te\u0107enja ki\u010dmene mo\u017edine i u zavisnosti od mesta lezije pacijeti \u010desto\u00a0 imaju simetri\u010dnu slabost svih ekstremiteta ili samo dojih ekstremiteta, razli\u010ditog stepena pa sve do te\u0161ke ili potpune oduzetosti. Postoji gubitak ose\u0107aja za dodir, temperaturne razlike, poreme\u0107aj mokrenja, defekacije i seksualnih funkcija, spazmi (bolni mi\u0161i\u0107ni gr\u010devi), zategnutost u mi\u0161i\u0107ima-spasticitet,. Mogu se javiti i mu\u010dnina, \u0161tucanje, povra\u0107anje, duple slike, vrtoglavica, gubitak sluha, pad kapka, trigeminalna neuralgija.<\/span><\/p>\n<p><strong>Kako se postavlja dijagnoza bolesti?<\/strong><\/p>\n<p><span style=\"font-weight: 400;\"><a href=\"https:\/\/euromedic.rs\/usluga\/specijalisticki-pregled-neurologa\/\">Pregledom neruologa<\/a> i primenom dopunskih dijagnosti\u010dkih procedura kojima se potvr\u0111uje ili isklju\u010duje dijagnoza neuromijelitis optika spaktra bolesti.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">MR endokranijuma (magnetna rezonanca glave ) ja\u010dine od 1,5-3.0 T sa primenom i.v. kontrastnog sredstva, kao i nalaz MR\u00a0 ki\u010dmene mo\u017edine vratnog i grudnog dela\u00a0 sa primena i.v. kontrastnog sredstva, uz\u00a0 jasno definisane neuroradiolo\u0161ke kriterijume koji se koriste kao dijagnosti\u010dki protokol.\u00a0<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Lumblana punkcija (LP)\u00a0 kojom se dobija likvor ( mo\u017edinsko-ki\u010dmena te\u010dnost) i detektovanje prisutva \u00a0 specifi\u010dnog biomarkera: anti AQP4 \/NMO-IgG at,\u00a0 ili\u00a0 anti MOGat,\u00a0 u serumu i likvoru.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Osim ove analize, istovremeno se uzorci likvora i krvi (serum) koriste i za\u00a0 odre\u0111ivanje drugih brojnih\u00a0 citobiohemijskih, imunolo\u0161kih, serolo\u0161kih pokazatelja (na HIV, na\u00a0 odre\u0111ene viruse, ujed krplja, malignitet, idetekciju oligoklonalnih IgG traka, odre\u0111ivanje anti tela na druge autoimune bolesti), a radi isklju\u010divanja drugih\u00a0 bolesti.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Vizuelni Evocirani Potencijali (VEP), ispituju funkciju opti\u010dkog nerva, u smislu postojanja ili isklju\u010denja opti\u010dkog neuritisa.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Magnetna rezonanca opti\u010dkog \u017eivca sa primenom i.v. kontrastnog sredstva.\u00a0<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Pregled oftalmolga i OCT (opti\u010dka koherentna tomografija).<\/span><\/p>\n<p><span style=\"font-weight: 400;\">\u010cesto su potrebni i drugi specijalisti\u010dki pregledi (kardiolog, reumatolog, pulmolog, imunolog, oftalmologa, i dr.)<\/span><\/p>\n<p><strong>Terapija u le\u010denju neurmijelitis optika spektra bolesti sastoji se iz:<\/strong><\/p>\n<p><span style=\"font-weight: 400;\">Terapija akutne faze bolesti: primena kortikosteroidne terapije u visokim dozama (&#8220;pulsna terapija&#8221;) intravenski tokom 3-5 dana u bolni\u010dkim uslovima, sa\u00a0 nastavakom le\u010denja kortikosteroidne terapije\u00a0 u vidu tableta, oralno. Kod te\u017eih oblika gde primena kortikosteroidne terapije nije dovela do pobolj\u0161anja, mo\u017ee se primeniti i terapijska izmena plazme (TIP) u bolni\u010dkim uslovima i specijalizovanim jedinicama.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Ukoliko izostane terapijski efekat\u00a0 i\u00a0 TIP,\u00a0 mo\u017ee se\u00a0 primeniti\u00a0 terapija ciklofosfamidom\u00a0 ili esterazni inhibitora u bolni\u010dkim uslovima.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">I preventivna terapija relapsnog oblika NMO spektra bolesti.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Prva linija: Azathioprin, Mycophenolat-mofetil \u00a0 (MMF),\u00a0 Rituximab .<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Druga linija: Methotrexat, Mitoxantron,Cyclosporin, Cyclophosphamide.\u00a0<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Nove terapijske opcije: Eculizumab,Inebilizumab, Tocilizumab, Satralizumab Citirizine,\u00a0 antihistaminic,&#8230;..<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Simptomatska terapija, obuhvata medikametni pristup le\u010denju, odnosno primenu terapije za\u00a0 brojne ve\u0107 navedene simptoma koji parate ovu bolest., kao i primena\u00a0 fizikalne terapije, psihoterapije,odnosno neurorehabilitacija bazirana na multidisciplinarnim\u00a0 rehabilitacionim programima, sa akcentom na individualni pristup svakom pacijetu.<\/span><\/p>\n<p><strong>Zasto je dobro odabrati Euromedik tim u proceduri\u00a0 ispitivanja i postavljanja dijagnoze\u00a0 NMO spektra bolesti?<\/strong><\/p>\n<p><span style=\"font-weight: 400;\">Zato \u0161to tim Euromedika \u010dine iskusni dobro edukovani lekari: neurolog, neuroradiolog, oftalmologa, reumatologa, imunologa, pulmologaa, fizijatra, psihijatar, i lekari drugih specijalnosti sa multidiciplinarnim prisutupom\u00a0 u dijagnostici\u00a0 i le\u010denju\u00a0 NMO spektra bolesti.\u00a0<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Zato \u0161to se u Euromediku sve potrebne dijagnosti\u010dke procedure i pregledi izvode na novim modernim i visoko kvalitetnim ure\u0111ajima,\u00a0 po visokim medicinskim i evropskim standardima, uz detaljno i adekvatno tume\u010denja nalaza, sa individualnim pristupom svakom pacijetu.<\/span><\/p>\n<p><span style=\"font-weight: 400;\">Zato \u0161to se u Euromediku u bolni\u010dkim uslovima\u00a0 uz profesionalan visoko edukovan medicinski kadara lekara i medicinskog osoblja, mo\u017ee primeniti terapija u akutnoj fazi bolesti koja zahteva dobru opremljenost i bolni\u010dke uslove pri primeni, kao i dalje pra\u0107enje pacijeta i primenu\u00a0 preventivne terapije\u00a0 NMO spektra\u00a0 bolesti.<\/span><\/p>\n<p>&nbsp;<\/p>\n","protected":false},"excerpt":{"rendered":"<p>Neromijelitis optika spektar bolesti ili NMO spektar bolesti (NMOSD od engl.\u00a0 neuromyelitis optica spectrum disorder)&#8230;<\/p>\n","protected":false},"author":1,"featured_media":6053,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"inline_featured_image":false,"footnotes":""},"categories":[484],"tags":[295,320],"class_list":["post-6051","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-neurologija","tag-neurologija","tag-neuromijelitis-optika"],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v23.2 - 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